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Mega os trigonum in progressive pseudorheumatoid dysplasia
1Children's Hospital Medical Center, 3333 Burnet Avenue, Cincinnati, OH 45229-3039, USA. oestreich.ae@chmcc.org
Pediatric Radiology
|January 31, 2002
Summary
Progressive pseudorheumatoid dysplasia (PPRD) can be distinguished from juvenile rheumatoid arthritis (JRA) by identifying a large and early-forming os trigonum. This imaging finding aids in accurate PPRD diagnosis.
Area of Science:
- Pediatric Orthopedics
- Radiology
- Rheumatology
Background:
- Progressive pseudorheumatoid dysplasia (PPRD) is a noninflammatory skeletal disorder.
- Accurate diagnosis is crucial to differentiate PPRD from juvenile rheumatoid arthritis (JRA).
Purpose of the Study:
- To identify distinguishing imaging features of PPRD.
- To assess the utility of the os trigonum in differentiating PPRD from JRA.
Main Methods:
- Retrospective review of ankle imaging in four pediatric patients diagnosed with PPRD.
- Analysis of os trigonum size and ossification timing.
Main Results:
- Abnormally enlarged os trigonum observed in all PPRD subjects.
- Early appearance or fusion of the os trigonum noted in two subjects.
Conclusions:
- A large and early-developing os trigonum is a key radiographic finding.
- This feature aids in the differential diagnosis between PPRD and JRA.