Diffuse "essential" normolipemic xanthomatosis

Most types of cutaneous xanthomas are associated with hyperlipidemic states. However, the diffuse normolipemic xanthomatoses have normal lipid blood levels but are often associated with serious hepatic disease or hematologic dyscrasias, especially multiple myeloma. A patient is presented who had "essential" diffuse normolipemic xanthomatosis unassociated with any sytemic disease, and displayed an unusual number of different types of lesions. His condition was clearly different from those of patients reported with xanthoma disseminatum.