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Spontaneous retrobulbar hemorrhage in type IV Ehlers-Danlos syndrome
Saad Shaikh1, Maria Braun, Joseph Eliason
1William Beaumont Hospital, Royal Oak, Michigan 48073, USA. saads@earthlink.net
Purpose:
To describe a case of spontaneous retrobulbar hemorrhage in type IV Ehlers-Danlos syndrome, a disorder characterized by vascular fragility and associated severe bleeding problems.
Methods:
Observational case report. Spontaneous unilateral retrobulbar hemorrhage in a 22-year-old man with type IV Ehlers-Danlos syndrome was documented by clinical and radiographic examination.
Results:
The retrobulbar hemorrhage was self-limited and resolved without visual sequelae.
Conclusion:
Spontaneous retrobulbar hemorrhage should be recognized as part of the spectrum of type IV Ehlers-Danlos syndrome, and clinicians must be alert to diagnosis and treatment of this vision-threatening problem.