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[Obstructive esophageal membrane in recessive dystrophic epidermolysis bullosa]
J M Ruíz-Molina1, C M Ortíz-Mendoza
1Departamento de Gastroenterología, División de Cirugía Oncológica, Instituto Nacional de Cancerología (México), Av. San Fernando No. 22, CP 14000, Delegación Tlalpan, México, DF.
Background:
Dysphagia is a rare complication of esophageal webs.
Objective:
To describe a patient with dystrophic epidermolysis bullosa who developed dysphagia produced by an esophageal web that simulated carcinoma.
Case Report:
A 26 year-old male with dystrophic epidermolysis bullosa developed severe dysphagia and subsequently aphagia secondary to an upper third esophageal obstruction. A (CT) scan showed a circumferential esophageal wall thickening of the affected area. The patient was submitted to surgical neck exploration with endoscopic assistance to identify the obstruction and a esophagotomy was carried on detecting a complete esophageal web that was excised.
Conclusions:
Esophageal web must be considered a cause of esophageal obstruction in patients with dystrophic epidermolysis bullosa.