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[Late discovery of Lafora disease: a family study]
O Messouak1, M Yahyaoui, M Benabdeljalil
1Service de Neurologie, Rabat.
Revue Neurologique
|April 9, 2002
Abstract:
Lafora disease is a progressive myoclonic epilepsy, Clinically defined by the association of myoclonic, epileptic fits and dementia. We report a case with an atypical Lafora disease, marked by delayed onset at 25 years of age, prolonged course, associated with secondary cognitive impairment and myoclonic features.