Low grade primary clear cell carcinoma of the sinonasal tract

Clear cell carcinoma of the salivary glands are rare tumors. Metastatic clear cell carcinoma from a primary in the adrenal glands to the head and neck area have been described in the literature. However, primary clear cell carcinoma of the paranasal sinuses have not been yet alluded to in the literature except in the paper of Newman (1993). We are presenting our experience and long term follow-up in the diagnosis and management of such a lesion in the nose and paranasal sinuses.