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Partial anomalous pulmonary venous connection of singular form
Yoshihiro Ko1, Hiromi Kurosawa, Kiyozo Morita
1Department of Cardiovascular Surgery, Jikei University School of Medicine, 3-19-18 Nishishinbashi, Minato-ku, Tokyo 105-8461, Japan.
The Japanese Journal of Thoracic and Cardiovascular Surgery : Official Publication of the Japanese Association for Thoracic Surgery = Nihon Kyobu Geka Gakkai Zasshi
|June 21, 2002
Summary
This study details a rare case of partial anomalous pulmonary venous connection in a child, where three of four pulmonary veins had abnormal connections. Unique surgery using autologous tissue successfully corrected these complex congenital heart defects.
Area of Science:
- Cardiology
- Pediatric Surgery
- Congenital Heart Disease
Background:
- Partial anomalous pulmonary venous connection (PAPVC) is a rare congenital heart defect.
- Accurate preoperative diagnosis can be challenging, potentially leading to surgical surprises.
- Understanding the spectrum of anomalous pulmonary venous connections is crucial for surgical planning.
Observation:
- A 3-year-old female presented with suspected left superior pulmonary venous connection and atrial septal defect.
- Intraoperative findings revealed a unique anomaly: only the right superior pulmonary vein connected to the left atrium; the other three connected anomalously to the coronary sinus or innominate vein.
- An enlarged coronary sinus was noted, and no atrial septal defect was present.
Findings:
- The patient exhibited a complex form of PAPVC with three anomalous pulmonary veins, hemodynamically approaching total anomalous pulmonary venous connection.
- A novel surgical approach utilizing autologous tissue was employed for the complex reconstruction.
- Successful surgical correction was achieved, with positive outcomes reported.
Implications:
- This case highlights the importance of thorough intraoperative assessment in managing complex congenital heart anomalies.
- The described surgical technique offers a potential solution for rare and complex cases of anomalous pulmonary venous connections.
- Further research into surgical strategies for PAPVC variations could improve patient outcomes.