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Klippel-Feil syndrome associated with posterior fossa dermoid cyst. Case report
José M González-Darder1, Rosana Feliu-Tatay, José V Pesudo-Martínez
1Department of Neurosurgery, Hospital General de Castellón, Spain. gonzalez_jos@gva.es
Neurological Research
|July 16, 2002
Abstract:
A patient with association of Klippel-Feil syndrome and posterior fossa dermoid cyst is presented. The patient, a 36-year-old man, presented with an acute obstructive hydrocephalus due to the cyst and exhibited the typical triad of the Klippel-Feil abnormality with short neck, low hairline implantation and limited neck motion along with a complex cervical vertebrae fusion. The anatomical and clinical features as well as the pathophysiology of this rare association are discussed after a review of the literature.