[DUCLOS LHERMITE DISEASE: REPORT OF ONE CASE AND LITERATURE REVIEW]
Abstract:
Lhermitte-Duclos disease (also known as dysplastic gangliocytoma of the cerebellum) is an unusual disorder, is now known to occur in young patients as a manifestation of Cowden disease. We report the case of a young male, 31 years old, with this unusual disease who was sugically treated for the neurologic neoplasia. And submitted to colonoscopic polypectomy for the hamartomatous colonic polyps.
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