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[Chiari type I malformation in children: presentation in 34 cases]
A Chartier1, A Martinot, P Dhellemmes
1Clinique de pédiatrie, hôpital Jeanne-de-Flandre, centre hospitalier et universitaire, 2, avenue Oscar-Lambret, 59037 Lille, France.
Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie
|September 11, 2002
Summary
Chiari I malformation is increasingly found incidentally in children. Systematic neurophysiological testing is crucial for evaluating both severe and mild cases, guiding surgical decisions.
Area of Science:
- Pediatric Neurology
- Neurosurgery
- Medical Diagnostics
Context:
- Incidental diagnoses of Chiari I malformation are rising in children.
- Understanding clinical presentations and the utility of neurophysiological studies is essential.
Purpose:
- To assess Chiari I malformation presentations in children.
- To determine the frequency of severe versus incidental forms.
- To evaluate neurophysiological investigations for surgical indications.
Summary:
- A retrospective study of 34 pediatric patients (1984-2000) revealed severe Chiari I malformation in 12%.
- Brainstem compression signs (41%), scoliosis (21%), and incidental findings (26%) were noted.
- Polysomnography identified sleep apnea in 50% of tested cases, with one incidental case requiring surgery.
Impact:
- The 12% incidence of severe Chiari I malformation warrants routine neurophysiological evaluation.
- These investigations aid in the initial assessment and ongoing management of Chiari I malformations, including less symptomatic presentations.