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MR imaging findings of spinal dural involvement with Wegener granulomatosis

Sait Albayram1, Osman Kizilkilie, Ibrahim Adaletli

  • 1Department of Radiology, The Cerrahpasa Medical School, 34300 Kocamustafapasa, Istanbul, Turkey.

AJNR. American Journal of Neuroradiology
|October 10, 2002
PubMed

Insights

Wegener granulomatosis rarely affects the brain or meninges. This case highlights a rare instance of Wegener granulomatosis involving the cervical spinal dura, with detailed MR imaging findings presented.

Area of Science:

  • Neurology
  • Rheumatology
  • Radiology

Background:

  • Wegener granulomatosis (WG), now known as granulomatosis with polyangiitis (GPA), is a rare systemic vasculitis.
  • Cranial and meningeal involvement in WG/GPA is infrequent, occurring in 2-8% of patients.

Observation:

  • Meningeal involvement in WG/GPA is seldom reported, particularly when limited to the dura mater.
  • Spinal dura mater involvement by WG/GPA is exceptionally rare.

Findings:

  • This report details a unique case of a 52-year-old male with WG/GPA.
  • The patient presented with involvement of the cervical spinal dura.
  • Detailed magnetic resonance (MR) imaging findings of this rare dural manifestation are provided.

Implications:

  • This case expands the understanding of WG/GPA's potential neurological manifestations.
  • Highlights the importance of considering WG/GPA in the differential diagnosis of isolated cervical dural lesions.
  • Emphasizes the utility of advanced imaging techniques like MR in diagnosing rare presentations of systemic vasculitis.

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