Primary intraventricular haemorrhage: a rare presenting feature of arteriovenous malformation in children

Ramesh C Parmar1, S B Bavdekar, A Goel

  • 1Department of Paediatrics, Seth GS Medical College and KEM Hospital, Mumbai.

Insights

Brain arteriovenous malformations (AVMs) rarely cause intraventricular hemorrhage in children. This study reports two pediatric cases successfully treated with steroids, anti-epileptic drugs, and embolization.

Area of Science:

  • Pediatric Neurology
  • Neurosurgery
  • Vascular Malformations

Background:

  • Arteriovenous malformations (AVMs) are complex vascular anomalies.
  • Intracranial hemorrhage is a known complication of AVMs, particularly in adults.
  • Primary intraventricular hemorrhage from pediatric AVMs is exceptionally rare.

Observation:

  • Two children, aged 11 and 13, presented with primary intraventricular hemorrhage.
  • This presentation is rare in pediatric populations.
  • Adult intracranial bleeds secondary to AVM rupture account for 3%.

Findings:

  • Both pediatric cases responded well to a multimodal treatment approach.
  • Therapeutic strategies included steroids, anti-epileptic drugs, and embolization.
  • Successful management of intraventricular hemorrhage in pediatric AVM.

Implications:

  • This study reports a previously undocumented presentation of pediatric brain AVM.
  • Early diagnosis and tailored therapy are crucial for favorable outcomes.
  • Further research is needed to understand pediatric AVM hemorrhage patterns.

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