Rmyoplasia congenita

Amyoplasia congenita is a rare congenital disorder. Here such a case along with right sided inguinal hernia in 3-day-old male baby is presented with a brief review of literature. A 3-day-old male baby was presented with multiple bony deformities with right sided inguinoscrotal swelling since birth. It was diagnosed as a case of amyoplasia congenita along with a right sided inguinal hernia. The baby was managed with physiotherapy and right sided herniorrhaphy was done at 2 months and 2 days of age.