Major coronary anomalies in childhood

Daniël De Wolf1, Tom Vercruysse, Bert Suys

  • 1Department of Paediatric Cardiology, Ghent University Hospital, De Pintelaan 185, 9000 Gent, Belgium. daniel.dewolf@rug.ac.be

Insights

Rare coronary artery anomalies in children, including ALCAPA, fistulas, and stenosis, can be accurately diagnosed using various methods. Prompt treatment for these conditions leads to favorable outcomes.

Area of Science:

  • Pediatric Cardiology
  • Congenital Heart Disease
  • Cardiovascular Imaging

Background:

  • Major coronary artery anomalies are infrequent in pediatric populations.
  • Understanding diagnostic features and therapeutic strategies is crucial for managing these rare conditions.

Purpose of the Study:

  • To evaluate historical, diagnostic, and therapeutic aspects of three coronary artery anomalies in children.
  • Focus on abnormal origin of the left coronary artery from the pulmonary artery (ALCAPA), coronary fistula, and coronary stenosis.

Main Methods:

  • Retrospective review of 33 pediatric cases with coronary artery anomalies.
  • Analysis included patient history, physical examination, ECG, X-ray, echocardiography, and angiography.
  • Therapeutic options and patient outcomes were systematically assessed.

Main Results:

  • ALCAPA cases exhibited characteristic echocardiographic findings.
  • Coronary artery fistulas were identified by murmurs and echocardiographic dilatations.
  • Coronary stenosis diagnosis was suggested by specific clinical presentations.

Conclusions:

  • Accurate diagnosis of rare pediatric coronary artery anomalies is achievable.
  • Early intervention and appropriate therapy are associated with good prognoses.
Abstract

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