Use of distraction osteogenesis techniques in skeletal dysplasias

The authors report the results of 63 operations performed on patients with skeletal dysplasias using the techniques of distraction osteogenesis. There were a total of 26 patients (16 males, 10 females) with a mean age of 12.5 years. The group had 13 different skeletal dysplasias. In 55 of 63 (87%) of the procedures, the objectives of surgery were achieved. The authors review their results with reference to the type of fixator used and the underlying diagnosis. Circular frames were associated with improved results. Spondylometaphyseal dysplasia and Jeune syndrome were the only dysplasias treated that were associated with significant complications.