[Case report of a primary pericollagen amyloidosis (author's transl)]

The authors report about a female patient, 59 years old, who was suffering from a stenosis of the cardia. A malignant process was suspected and an operative treatment was planed. During the preoperative internal examinations a low voltage in the ECG was found so that an amyloidosis was suspected. This was proved by biopsy of the mucosa of the rectum. A chronic suppurative disease could not be found, it was then assumed that the patient is suffering from a "primary pericollagen amyloidosis". Because a splitting of the stenosis through the esophagoscope the biopsy showed no malignancy, but congo-red positive material around collagen tissue. This seldom disease, the differential-diagnosis and the possibilities of treatment are discussed. Under symptomatic therapy the patient is doing well 2 years since.