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Paroxysmal nocturnal hemoglobinuria arising from Fanconi anemia
Linda Wainwright1, Robert A Brodsky, Linda K Erasmus
1University of the Witwatersrand, Chris-Hani-Baragwanath Hospital, Johannesburg, South Africa. sjaspan@iafrica.com
Journal of Pediatric Hematology/Oncology
|February 7, 2003
Abstract:
The progress of a female child with African type Fanconi anemia that evolves in time into paroxysmal nocturnal hemoglobinuria is described. Modern diagnostic methods are used to confirm this process. A discussion of possible mechanisms ensues.