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Left Atrial Stenosis Induced Pulmonary Venous Arterialization and Group 2 Pulmonary Hypertension in Rat
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Idiopathic calcific constrictive pericarditis causing pulmonary stenosis associated with a ventricular septal defect

Shao-Ju Chien1, Chi-Di Liang, Sheung-Fat Ko

  • 1Department of Pediatric Cardiology, Chang Gung Children's Hospital, 123 Ta-Pei Road, Niao Sung Hsiang, Kaohsiung County 833, Taiwan.

Journal of Clinical Ultrasound : JCU
|April 15, 2003
PubMed

Insights

This case report details a rare instance of pulmonary stenosis due to calcific constrictive pericarditis in a patient with a ventricular septal defect. Surgical intervention led to a positive outcome, resolving symptoms and improving cardiac function.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Cardiovascular Surgery

Background:

  • Congenital heart defects and pericardial diseases can present complex diagnostic challenges.
  • Pulmonary stenosis and ventricular septal defects are known congenital abnormalities.
  • Constrictive pericarditis, particularly calcific, is a less common cause of significant hemodynamic compromise.

Observation:

  • A 16-year-old male presented with progressive dyspnea, cyanosis, fatigue, and edema.
  • Initial echocardiography suggested Tetralogy of Fallot.
  • Chest radiography and CT revealed calcific constrictive pericarditis with pulmonary stenosis.

Findings:

  • Cardiac catheterization confirmed calcific constrictive pericarditis and pulmonary stenosis.
  • The patient had an associated congenital ventricular septal defect.
  • This represents the first reported case of this specific combination of conditions.

Implications:

  • Surgical pericardiectomy and ventricular septal defect repair can effectively manage this rare condition.
  • Prompt diagnosis and intervention are crucial for favorable patient outcomes.
  • Highlights the importance of considering pericardial disease in complex pediatric cardiac presentations.

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