ALCAPA in an adult with preserved left ventricular function
Craig H Selzman1, Michael A Zimmerman, David N Campbell
1Division of Cardiothoracic Surgery, University of Colorado Health Sciences Center, Denver, CO 80262, USA. craig.selzman@uchsc.edu
Insights
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital defect. This case highlights a rare adult presentation with preserved heart function, emphasizing the need for timely diagnosis and surgical repair.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Adult Congenital Heart Disease
Background:
- Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is the most frequent congenital coronary anomaly.
- If left untreated, ALCAPA has a high mortality rate, with nearly 90% of patients dying within the first year of life.
Observation:
- This report details a rare case of ALCAPA in a 23-year-old female.
- The patient presented with completely preserved left ventricular function, an unusual finding for this condition.
Findings:
- The case underscores the potential for adult presentation of ALCAPA.
- Review of the literature examines the mechanisms behind this atypical presentation and discusses therapeutic strategies for adult patients.
Implications:
- Early diagnosis and surgical correction are crucial for improving outcomes in patients with ALCAPA.
- This case expands the understanding of ALCAPA presentations in adults and informs clinical management strategies.
Abstract:
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is the most common congenital coronary artery defect. Left uncorrected, nearly 90% of patients will die within one year. Without surgical repair, surviving patients are subjected to risks of myocardial ischemia with global cardiomyopathy, chronic mitral regurgitation, and sudden death. We report a case of ALCAPA in a 23-year-old female with completely preserved left ventricular function. This article reviews the mechanism of this unusual presentation as well as the therapeutic options for adults presenting with ALCAPA.
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