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Pseudotumor cerebri associated with Sjögren's syndrome
Dinu Stanescu1, Bahram Bodaghi, Du Le Thi Huong
1Department of Ophthalmology, Pitié-Salpétrière Hospital, Paris, France.
Purpose:
To report a case of papilledema and pseudotumor cerebri developed in association with Sjögren's syndrome.
Methods:
Case-report of a 38-year-old woman with history, imaging and histology confirming the diagnosis of both pseudotumor cerebri and Sjögren's syndrome who presented with bilateral decrease of vision.
Results:
Papilledema associated with pseudotumor cerebri was observed in both eyes. The patient's visual acuity improved transiently with the administration of intravenous steroids and cyclophosphamide; subsequently she needed a ventriculoperitoneal shunt.
Conclusion:
Sjögren's syndrome should be considered in the different etiologies of pseudotumor cerebri. The major improvement with corticosteroids and ventriculoperitoneal shunt makes prompt diagnosis essential.