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[An unusual chronic microvasculitis: Goodpasture's syndrome with late myocardial involvement]
R Mori1, A G Corvaglia, A Frustaci
1Istituto di Clinica medica, Università Cattolica del Sacro Cuore, Roma.
Recenti Progressi in Medicina
|November 1, 1992
Abstract:
We describe a disease, started in a female young adult patient as an apparent pulmonary siderosis, followed nine years later by an extracapillary proliferative nephritis, which developed to uremia in a few months. Later an intra-myocardial vasculitis, responsible of heart failure, appeared. Immune-histochemistry and serological tests exclude a disease mediated by anti-GMB antibodies, and pathologic features suggest a vasculitis mainly affecting lungs and kidneys.