[Benign concentric annular macular dystrophy: two cases]

We present two cases of two sisters with the presumed diagnosis of benign concentric annular macular dystrophy. Age was 16 and 22 years old respectively. They presented with decrease in visual acuity and annular atrophy of the macular retinal pigment epithelium. The fluorescein angiography showed <> pattern and the electrophysiologic tests were normal.

The prognosis of this dystrophy is fairly good, therefore it is important to make an accurate diagnosis to be able to distinguish it from others entities, mainly those presenting <> pattern in fluorescein angiography. We emphasize the usefulness of fluorescein angiography and electrophysiologic test (electroretinogram and electrooculogram).