[Epithelioid renal angiomyolipoma: benign or malignant tumor?]

Angiomyolipoma is a well-known rare soft tissue tumor involving the kidneys, liver and other organs. Long believed to be a benign hamartoma, angiomyolipoma is now considered a neoplasm that arises from perivascular epithelioid cell. Epithelioid angiomyolipoma is a rare variant of angiomyolipoma characterized by epithelioid cells that mimic renal cell carcinoma and is potentially malignant. Immunoreactivity with HMB45 is helpful for its identification. We report the computed tomographic and histologic findings in a 36 years old woman with epithelioid angiomyolipoma and lymph node involvement.