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Total anomalous pulmonary venous return with associated patent ductus arteriosus. Two cases with successful
Insights
Successful surgical repair of total anomalous pulmonary venous return with a large patent ductus arteriosus is rare but possible. This study details two successful cases, highlighting long-term survival possibilities for this complex congenital heart defect.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Surgical Innovation
Background:
- Total anomalous pulmonary venous return (TAPVR) with a large patent ductus arteriosus (PDA) presents unique, often fatal, hemodynamic challenges.
- Long-term survival for patients with this complex congenital heart defect is historically rare.
- Successful surgical intervention for this specific combination requires careful consideration of anatomical and physiological factors.
Observation:
- Two patients, aged five and 18 years, presented with supracardiac TAPVR and a large PDA.
- Both patients underwent successful surgical repair, demonstrating the feasibility of intervention.
- The 18-year-old patient also had Noonan syndrome, adding a layer of complexity and interest.
Findings:
- Successful surgical repair of supracardiac TAPVR and large PDA is achievable.
- This approach can lead to long-term survival in select pediatric and adult cases.
- The presence of genetic syndromes like Noonan syndrome can coexist and be managed alongside cardiac repair.
Implications:
- This study offers hope and a potential surgical pathway for patients with previously considered inoperable conditions.
- It underscores the importance of individualized surgical planning for complex congenital heart disease.
- Further research into long-term outcomes and management strategies for TAPVR with PDA, especially in the context of genetic syndromes, is warranted.
Abstract:
A large patent ductus arteriosus associated with total anomalous pulmonary venous return results in a unique hemodynamic pattern, and long-term survival has been rare. Two patients, aged five and 18 years, underwent successful surgical repair of supracardiac total anomalous pulmonary venous return and an associated large patent ductus arteriosus. The association of the Noonan syndrome in the 18-year-old woman is of additional interest.