[A case of primary acinic cell tumor of the trachea]

A 62-year-old woman complained cough and hemosputum. Chest X-ray film and thoracic computed tomography revealed tumor shadow, localizing in the upper trachea, measuring 2 x 1 cm. Through a median sternotomy, resection of the trachea of 4 cartilagous rings was made, followed by end-to-end anastomosis. Fixing of tracheal anastomosis was performed for 2 weeks using SOMI brace. The size of tumor was 1.3 cm in diameter. Histologically, nodular tumor foci were seen close to the normal trachea gland, localing in tracheal mucosa. Tumor cells with basophilic cytoplasma developed acinical structure. Postoperative course was uneventful. This patient is alive 42 months after resection. This disease is extremely rare, we have found only 4 reported cases including our case in the world literature and only 2 cases in the Japanese literature.