[Sézary syndrome with rapidly progressing pulmonary lymphoma in a child]

A 7 year old boy with a prior history of T-cell acute lymphoblastic leukemia developed Sezary syndrome or cutaneous lymphoma of T-lymphocytes (CLTL). His course was rapidly progressive and fatal with the primary manifestation being pulmonary lymphoma. This patient is one of the youngest with CLTL to manifest extracutaneous involvement.