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Updated: Jul 15, 2026
06:08
A Novel Method: Super-selective Adrenal Venous Sampling
Published on: September 15, 2017
Pediatric extraadrenal paraganglioma
Tanya M Tekautz1, Charles B Pratt, Jesse J Jenkins
1Department of Hematology-Oncology, St. Jude Children's Research Hospital, Memphis, TN 38105-2794, USA.
Journal of Pediatric Surgery
|October 3, 2003
Summary
Pediatric extraadrenal paraganglioma is rare, often presenting in the retroperitoneum and head/neck. Complete surgical resection offers the best outcome for these rare pediatric tumors.
Area of Science:
- Pediatric Oncology
- Surgical Pathology
- Rare Tumors
Background:
- Pediatric paraganglioma is a rare condition.
- Extraadrenal paraganglioma in children is not well-characterized.
Purpose of the Study:
- To characterize pediatric extraadrenal paraganglioma.
- To evaluate clinical presentation, treatment, and outcomes.
Main Methods:
- Retrospective review of medical records and pathology samples.
- Study period: December 1978 to September 2000.
- Eight pediatric patients with extraadrenal paraganglioma were identified.
Main Results:
- Tumors most commonly arose in the retroperitoneum and head/neck.
- Diagnosis was not suspected at presentation in any patient.
- Gross total resection led to disease-free survival in 4 of 5 patients; neoadjuvant therapy aided resection of unresectable tumors.
Conclusions:
- Pediatric extraadrenal paraganglioma typically presents in the retroperitoneum and head/neck.
- Diagnosis is often delayed.
- Surgical resection is the primary treatment, with favorable outcomes after complete removal.
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