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Updated: Aug 30, 2026

Imaging Features of Systemic Sclerosis-Associated Interstitial Lung Disease
Published on: June 16, 2020
Evaluation and management of pulmonary hypertension in systemic sclerosis
Ioana R Preston1, Nicholas S Hill
1Division of Pulmonary, Critical Care and Sleep, Tufts-New England Medical Center and Tufts School of Medicine, Boston, Massachusetts 02111, USA.
Abstract:
This review summarizes the most recent studies on pulmonary hypertension related to systemic sclerosis, emphasizing new insights into pathophysiology, identification of new markers, and advances in the diagnosis and treatment of this complication that greatly worsens the prognosis of patients with systemic sclerosis.
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