[Choledochal cyst: a 10-year experience]

L H Pereira1, J M Bustorff-Silva, L Sbraggia-Neto

  • 1Universidade Estadual de Campinas (UNICAMP), Campinas, SP, Brazil.

Jornal De Pediatria
|December 4, 2003
PubMed

Insights

Early diagnosis and surgical resection of choledochal cysts lead to good outcomes. Most pediatric patients achieved symptom-free recovery after cyst resection and hepaticojejunostomy, though some developed chronic pancreatitis.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Medical Imaging

Background:

  • Choledochal cysts are rare congenital biliary abnormalities predominantly affecting female infants and children.
  • Optimal outcomes for choledochal cysts rely on timely diagnosis, complete surgical excision, and reconstruction with hepaticojejunostomy.

Purpose of the Study:

  • To assess the long-term outcomes of 18 patients who underwent surgical management for choledochal cysts over a decade.

Main Methods:

  • A retrospective chart review was conducted on 18 pediatric patients diagnosed with choledochal cysts.
  • Surgical interventions included cyst resection and Roux-en-Y hepaticojejunostomy for most cases.
  • Diagnostic modalities utilized were ultrasonography and endoscopic retrograde cholangio-pancreatography.

Main Results:

  • The patient cohort ranged from 20 days to 13 years, with 83% being female.
  • Common presenting symptoms included jaundice (83%), dark urine (61%), and abdominal pain (50%).
  • Postoperative follow-up revealed 86% of patients were symptom-free, while 14% developed chronic pancreatitis. Two early deaths (11%) occurred due to liver function deterioration.

Conclusions:

  • Surgical management, including cyst resection and Roux-en-Y hepaticojejunostomy, offers a favorable prognosis for most pediatric choledochal cyst patients.
  • While effective, potential long-term complications such as chronic pancreatitis warrant continued monitoring.