[Primary pulmonary hemangiopericytoma: 2 new cases]

Area of Science:

• Thoracic Surgery
• Oncology
• Pathology

Background:

• Primary pulmonary hemangiopericytoma is a rare neoplasm.
• Understanding its clinical behavior and optimal management is crucial.

Observation:

• Two new cases of resected primary pulmonary hemangiopericytoma are presented.
• A review of literature cases from 1954-2002 is included.
• Both cases presented with delayed symptoms and large masses.

Findings:

• Malignant hemangiopericytoma, closely related to solitary fibrous tumors, was confirmed via histology and immunohistochemistry.
• Despite radical resection, both patients experienced distant metastases and succumbed to the disease.
• Pulmonary hemangiopericytoma is characterized by slow growth, delayed symptoms, and distinct metastatic patterns compared to lung cancer.

Implications:

• Radical surgical resection is the primary treatment modality.
• Adjuvant chemotherapy and radiotherapy may offer prognostic benefits.
• Long-term follow-up (10-20 years) is essential due to the tumor's slow-growing nature and potential for late recurrence.