Coronary arterial compression treated by stenting after replacement of the mitral valve in a child

Area of Science:

• Cardiology
• Pediatric Cardiology
• Interventional Cardiology

Background:

• Shone's syndrome is a rare congenital heart defect.
• The patient had a history of aortic coarctation treated in infancy.

Observation:

• The patient developed severe sub-aortic stenosis and moderate mitral valvar stenosis.
• Mitral valve replacement with a mechanical prosthesis and sub-aortic shelf resection were performed.

Findings:

• Post-operative myocardial ischemia was observed.
• Coronary angiography revealed mechanical prosthesis compression of the circumflex artery.
• Successful balloon angioplasty and stenting of the circumflex artery were performed.

Implications:

• This case highlights a rare complication of mechanical valve prosthesis in pediatric Shone's syndrome.
• Interventional cardiology techniques can effectively manage prosthesis-induced coronary artery compression.
• Timely diagnosis and intervention are crucial for favorable outcomes in complex congenital heart disease.