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Bourneville's tuberous sclerosis associated with double outlet right ventricle and infundibular pulmonary stenosis
N B Raut1, J B Norton, A A Patil
1University of Arkansas.
Abstract:
The cardiac manifestation usually associated with tuberous sclerosis is rhabdomyoma of the heart. We report a rare association with cyanotic congenital heart disease in the form of double outlet right ventricle with infundibular pulmonary stenosis.