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Spontaneous rupture of a right atrial angiosarcoma and cardiac tamponade
Ricardo Barros Corso1, Nadja Kraychete, Sidnei Nardeli
1Serviço de Cirurgia Cardíaca Cardiocirúrgica, Serviço de Cardiologia Clínica Cardiointensiva, Hospital Santa Izabel, Santa Casa de Misericórdia, Salvador, BA, Brazil.
Abstract:
Primary cardiac angiosarcoma is a rare disease of difficult diagnosis and poor prognosis frequently associated with recurring hemopericardium. We report the case of a 30-year-old female with a right atrial angiosarcoma and spontaneous rupture to the pericardial cavity, who was diagnosed during an emergency exploratory thoracotomy, whose indication was cardiac tamponade. This is the 8th case reported in the literature. Clinical findings are discussed and a literature review is provided.
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