Atrial septal defect in apical hypertrophic cardiomyopathy associated with coronary spasm

Insights

Apical hypertrophic cardiomyopathy (HCM) with atrial septal defect (ASD) and coronary spasm is rare. This case report details successful diagnosis and surgical treatment, alleviating patient symptoms.

Area of Science:

  • Cardiology
  • Cardiovascular Diseases
  • Cardiac Surgery

Background:

  • Apical hypertrophic cardiomyopathy (HCM) is a recognized myocardial disease.
  • The rare co-occurrence of HCM with atrial septal defect (ASD) and coronary spasm presents diagnostic and therapeutic challenges.

Observation:

  • A 62-year-old male presented with congestive heart failure.
  • The patient exhibited apical HCM complicated by coronary spasm and a secundum-type ASD.

Findings:

  • Diagnostic imaging, including transthoracic and transesophageal echocardiography, alongside cardiac catheterization, proved crucial.
  • Medical management with calcium channel blockers for coronary spasm and surgical patch closure for ASD were successfully implemented.

Implications:

  • This case highlights the importance of comprehensive diagnostic approaches for complex cardiac conditions.
  • Successful surgical intervention and medical management can effectively alleviate symptoms in patients with coexisting apical HCM, ASD, and coronary spasm.

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