Multiple congenital coronary artery fistulae draining into the left ventricle

Carlos Felipe Barrera-Ramírez1, Jesús Jiménez-Mazuecos, Pilar Portero Pérez

  • 1Interventional Cardiology Unit, Cardiovascular Institute, Hospital Clínico San Carlos, Plaza Cristo Rey s/n, 28040, Madrid, España. carlosfbarrera@yahoo.com

Insights

Multiple coronary artery-left ventricular fistulas are rare. This case highlights a diffuse presentation in an elderly woman, making surgical or transcatheter interventions unsuitable.

Area of Science:

  • Cardiology
  • Vascular Medicine
  • Congenital Heart Disease

Background:

  • Coronary artery fistulas (CAFs) are abnormal connections between a coronary artery and a cardiac chamber.
  • While CAFs are rare, multiple fistulas involving the left ventricle are exceptionally uncommon.
  • This case focuses on a rare presentation of diffuse coronary artery-cardiac chamber communications.

Observation:

  • An elderly woman presented with symptoms suggestive of coronary artery disease.
  • Diagnostic coronary angiography revealed multiple, diffuse fistulous communications between coronary arteries and the left ventricle.
  • The widespread nature of the fistulas precluded standard interventional approaches.

Findings:

  • The patient was diagnosed with multiple diffuse coronary artery-left ventricular fistulas.
  • Angiographic findings confirmed the extensive and widespread nature of the arteriovenous communications.
  • The diffuse pattern of the fistulas presented a significant management challenge.

Implications:

  • The case underscores the importance of comprehensive angiographic evaluation for complex coronary artery anomalies.
  • Management strategies for diffuse coronary artery fistulas require careful consideration due to limitations of conventional treatments.
  • This presentation suggests that conservative management may be the only option for certain extensive fistula cases.

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