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Recurrent extraperitoneal low grade leiomyosarcoma with unusual localization.
E S Guvendag Guven1, S Guven, S Esin
1Department of Obstetrics and Gynecology, Hacettepe University Faculty of Medicine, Ankara, Turkey.
European Journal of Gynaecological Oncology
|June 3, 2004
Summary
Recurrent low-grade leiomyosarcoma in the pelvis is rare. This case highlights a paravaginal mass initially diagnosed as leiomyoma, later confirmed as leiomyosarcoma after recurrence.
Area of Science:
- Gynecologic Oncology
- Surgical Pathology
Background:
- Primary extragenital leiomyosarcomas are uncommon, particularly in pelvic locations.
- Leiomyosarcomas can arise in various soft tissues, presenting diagnostic challenges.
Observation:
- A 33-year-old woman presented with pelvic pain, dyspareunia, and gait disturbance.
- A recurrent paravaginal mass was noted three years after initial excision of a mass initially diagnosed as leiomyoma.
Findings:
- Histological examination confirmed the recurrent paravaginal mass as a low-grade leiomyosarcoma.
- The tumor recurred at the original tumor bed despite maximal excision.
Implications:
- This case underscores the importance of vigilant follow-up for paravaginal masses, even those initially presumed benign.
- Accurate pathological diagnosis and consideration of leiomyosarcoma in recurrent pelvic masses are crucial for appropriate management.