Pseudomyxoma extraperitonei occurring 35 years after appendicectomy: a case report and review of literature

Mamoon H Solkar1, Naveed M Akhtar, Zareen Khan

  • 1Department of Surgery, Darent Valley Hospital, Darenth Wood Road, Dartford Kent, DA2 8DA, UK. mamoonsolkar@hotmail.com

Abstract

Insights

Pseudomyxoma extraperitonei, a rare condition of mucinous implants outside the peritoneum, was observed after a 35-year incubation period following appendicectomy for a perforated appendix.

Area of Science:

  • Gastroenterology
  • Oncology
  • Surgical Pathology

Background:

  • Pseudomyxoma peritonei is a rare mucinous ascites condition, typically from appendiceal or ovarian tumors.
  • Pseudomyxoma extraperitonei is an extremely rare variant with retroperitoneal mucinous implants and no intraperitoneal involvement.

Purpose of the Study:

  • To report a unique case of pseudomyxoma extraperitonei.
  • To highlight the exceptionally long incubation period associated with this rare condition.

Main Methods:

  • Case report of a 57-year-old male patient.
  • Review of medical history including appendicectomy for a perforated appendix.

Main Results:

  • The patient developed pseudomyxoma extraperitonei.
  • The condition manifested 35 years after the initial appendicectomy.

Conclusions:

  • Pseudomyxoma extraperitonei is a recognized, albeit rare, clinical entity.
  • This case represents the longest documented incubation period of 35 years for pseudomyxoma extraperitonei.

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