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Updated: Aug 12, 2026

Assessment of Neuromuscular Function Using Percutaneous Electrical Nerve Stimulation
Published on: September 13, 2015
Cardiac function tests in neuromuscular diseases
Deepak Bhakta1, William J Groh
1Department of Medicine, Krannert Institute of Cardiology, Indiana University School of Medicine, 1800 North Capitol, Room E406, Indianapolis, IN 46202, USA.
Insights
Early cardiac function tests are crucial for identifying myocardial involvement in neuromuscular diseases, aiding in understanding disease mechanisms and limiting progression before severe symptoms arise.
Area of Science:
- Cardiology
- Neurology
- Genetics
Background:
- Neuromuscular diseases frequently involve the heart, contributing significantly to patient morbidity and mortality.
- Early detection of cardiac complications is vital for effective management and improved patient outcomes.
Purpose of the Study:
- To review diagnostic tests for cardiac involvement in neuromuscular diseases.
- To provide management guidelines for identified cardiac complications.
Main Methods:
- Literature review of cardiac assessment tools.
- Analysis of current clinical guidelines for cardiac management in neuromuscular disorders.
Main Results:
- Various cardiac function tests can detect myocardial involvement.
- Timely intervention can potentially slow disease progression.
Conclusions:
- Cardiac screening is essential for patients with neuromuscular diseases.
- Established guidelines aid in managing cardiac complications effectively.
Abstract:
Myocardial involvement is a known complication of neuromuscular diseases and is a leading cause of morbidity and mortality in these disorders. Identifying patients early using cardiac function tests helps understand the mechanisms underlying cardiac involvement and may help limit the progression of cardiac disease before the onset of significant symptoms and limitation. This article outlines the tests available to assess cardiac involvement associated with neuromuscular diseases and offers guidelines for management once they are discovered.
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