Treatment of unilateral lambdoid synostosis with cranial distraction

Yuzo Komuro1, Akira Yanai, Ayato Hayashi

  • 1Department of Plastic and Reconstructive Surgery , Juntendo University School of Medicine, Tokyo, Japan. komuro@med.juntendo.ac.jp

Insights

Unilateral lambdoid synostosis, a rare craniosynostosis, causes skull deformities. Surgical correction using distraction osteogenesis and barrel stave osteotomy effectively improved cranial shape in an infant patient.

Area of Science:

  • Neurosurgery
  • Pediatric Plastic Surgery
  • Craniofacial Surgery

Background:

  • Posterior plagiocephaly diagnosis and treatment remain controversial.
  • Unilateral lambdoid synostosis is a rare craniosynostosis causing ipsilateral occipital flattening.
  • Early and accurate diagnosis is crucial for effective management.

Observation:

  • An 8-month-old infant presented with right occipital flattening, mastoid bulge, and frontal prominence.
  • Facial examination revealed anteroinferior displacement of the right auricle.
  • Skull radiography and 3D CT confirmed premature fusion of the right lambdoid suture.

Findings:

  • The patient was diagnosed with unilateral lambdoid synostosis.
  • Surgical intervention involved distraction osteogenesis and barrel stave osteotomy.
  • Post-operative assessment at 1 year showed significant improvement in cranial symmetry.

Implications:

  • This case highlights the successful surgical management of a rare craniosynostosis.
  • Distraction osteogenesis combined with barrel stave osteotomy is an effective treatment.
  • Improved surgical outcomes can enhance quality of life for affected children.

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