[Rhabdomyolipoma of the right ventricle]

Echocardiography on a 29-year-old woman with exercise-unrelated tightness in the left chest for some months demonstrated an echo-dense space-occupying lesion in the outflow tract of the right ventricle (RV). Nuclear magnetic imaging revealed an ovular, fat-containing tumour, 3 x 2 x 2 cm in size. Because of threatened obstruction of the RV outflow tract removal of the tumour under cardiopulmonary bypass was undertaken. But complete removal was possible only by resecting a 2 x 3 cm area of the anterior wall of the RV, the resulting defect being covered with a Goretex patch. Histological examination identified the tumour as a rhabdomyolipoma. The patient was free of symptoms 1 year postoperatively.