Related Experiment Videos
[Gaucher's disease uncovered late]
Fatma Ben Said1, Sondes Mseddi, Nada Ben Aribia
1Service et Laboratoire d'hématologie, CHU Hédi Chaker SFAX.
Abstract:
Gaucher's disease is an uncommon inborn recessive autosomal disease, due to a deficient activity of the lysosomal enzyme beta glucocerebrosidase. This disease is usually diagnosed in the first or second decade of life with the arising of bone pains, splenomegaly and hemorragic manifestations due to thrombocytopenia. When the enlarged spleen is not evident, or after splenectomy, patients may be mis-identified as having Gaucher's disease. We present here two cases of elderly patients aged 70 and 46 years respectively, in whom the disease was a surprising finding of bone marrow examination, during check up for pancytopenia.
Related Concept Videos
Lysosomal Hydrolases
Barrett Esophagus-I: Introduction
This constant acid exposure transforms the esophagus's pink mucosal lining (stratified squamous epithelium) into a type of lining more similar...
Glucose Transporters
Facilitated diffusion-glucose transporters (GLUTs) are encoded by the solute-linked carrier (SLC) family 2, subfamily A gene family, or SLC2A. The 14 GLUT protein members are distributed into three classes:
Type II Diabetes Mellitus III: Clinical Manifestations and Diagnosis
Huntington Disease l: Introduction
Diabetes: Symptoms, Diagnosis, and Complications