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[Currarino triad: a case report].
Hiroaki Matsumoto1, Kanehisa Kohno, Daizou Ishii
1Department of Neurosurgery, Ehime Prefectural Central Hospital, Japan. c-hmatsumoto@eph.pref.ehime.jp
No Shinkei Geka. Neurological Surgery
|October 7, 2004
Summary
Currarino triad, a rare condition, involves sacral and spinal anomalies. This case highlights successful surgical correction in an infant using posterior sagittal anorectoplasty (PSARP) for a complex presentation.
Area of Science:
- Pediatric Surgery
- Neuroscience
- Medical Genetics
Background:
- Currarino triad is a rare congenital disorder characterized by a specific combination of anomalies.
- It typically includes a sacral defect, anorectal malformation, and a presacral mass, often a teratoma or anterior meningocele.
- Associated spinal cord abnormalities like tethered cord are common.
Observation:
- A newborn female presented with symptoms of intestinal obstruction including vomiting, abdominal distension, and constipation.
- Initial management involved a diverting colostomy at one month of age.
- The patient was diagnosed with Currarino triad, featuring anterior sacral meningocele, mature teratoma, sacral deformity, anorectal stenosis, and tethered cord.
Findings:
- A single-stage posterior sagittal anorectoplasty (PSARP) was performed at 8 months of age.
- This procedure successfully achieved simultaneous extirpation of the teratoma, excision of the meningocele, spinal cord untethering, and anorectoplasty.
- The surgical intervention was completed without complications.
Implications:
- Magnetic Resonance Imaging (MRI) is crucial for identifying spinal and sacral anomalies in infants with intractable constipation.
- Combined pediatric and neurosurgical management is recommended for optimal outcomes in Currarino triad cases.
- Early and comprehensive surgical intervention can effectively address the complex anatomical challenges of Currarino triad.