Congenital lipoblastoma of the scalp
Vivekanand Singh1, Rama Raju, Meenal Singh
1Pathology, Children's Mercy Hospital, Kansas City, Missouri 64108, USA.
Insights
Congenital lipoblastoma, a rare tumor in infants, can present as a large scalp mass. This case highlights successful surgical resection and a 3-year recurrence-free outcome for this pediatric tumor.
Area of Science:
- Pediatric Oncology
- Surgical Pathology
Background:
- Lipoblastoma is a rare benign tumor of infancy and early childhood.
- Typically found in the trunk and extremities, it rarely occurs in the head and neck region.
Observation:
- A congenital lipoblastoma of the scalp is described in an infant, presenting as a rapidly growing 15x15x10 cm mass.
- The tumor, initially at the bregma, extended to the left upper eyelid and eyebrow.
Findings:
- Surgical resection was performed in two stages: scalp mass removal and excision of the eyelid extension.
- Histopathology confirmed lobular adipose tissue with fibrous septae, consistent with lipoblastoma.
Implications:
- This case represents the first reported instance of congenital lipoblastoma of the scalp.
- Successful surgical management resulted in no recurrence at 3-year follow-up, suggesting favorable outcomes for this rare presentation.
Abstract:
Lipoblastoma is a unique tumor of infancy and early childhood that can occur congenitally. It commonly occurs in trunk and extremities, but also rarely in head and neck. We have not encountered any report of congenital lipoblastoma of scalp in published literature. Here we describe the case of an infant who presented with a rapidly growing large scalp mass that measured 15 x 15 x 10 cm. At birth, the mass was located on the bregma but progressed to extend into the left upper eyelid and eyebrow. The mass was resected in two stages: the first stage consisted of resecting the scalp mass and the second stage consisted of excising the eyelid extension of the lesion. The histology of both resection specimens was similar and showed lobular adipose tissue separated by fibrous septae, which was consistent with a lipoblastoma. The child is free of recurrence at follow-up 3 years after the resection.
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