Obstructive jaundice caused by polypoid inflammatory granuloma in a consanguineous case

Granuloma in the biliary system is a rare condition. The majority of the reported cases concern postsurgical granuloma. We note a patient with obstructive jaundice due to inflammatory granuloma in whom a filling defect was found at the bifurcation of the common hepatic duct by preoperative cholangiography. There have been no reported cases with similar findings. In addition to these features, this case was further characterized by consanguinity, repeated spontaneous abortions, and severe vascular lesions found in many organs that suggested the presence of a hereditary defect.