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Published on: September 9, 2016
Coronary and valve angiodysplasia unmasked by eosinophilic vasculitis and endomyocarditis
Cristina Chimenti1, Elisabetta La Penna, Maurizio Pieroni
1Cardiology Department, Catholic University, Largo A. Gemelli 8, 00168 Rome, Italy.
Abstract:
A previously unreported case of a complex congenital cardiac anomaly consisting of coronary and valvular angiodysplasia, complicated by an eosinophilic endomyocardial disease, is described. The disorder presented clinically with congestive heart failure, which was characterized by evidence of floating masses causing severe pulmonary stenosis and dysfunction of the mitral and aortic valves. Symptoms of cardiac failure disappeared following pulmonary valve replacement and steroid therapy.
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