Infantile fibrous dysplasia of the mandible

Insights

This study presents a rare case of mandibular fibrous dysplasia in a 12-week-old infant. Early surgical intervention was successful, with no observed recurrence at 6 months.

Area of Science:

  • Pediatric Oncology
  • Craniofacial Surgery
  • Skeletal Dysplasias

Background:

  • Fibrous dysplasia of the craniofacial skeleton is a rare benign bone neoplasm.
  • Infantile presentation (<1 year) of this condition is exceptionally uncommon.

Observation:

  • A case of mandibular fibrous dysplasia in a 12-week-old infant is described.
  • The neoplasm presented as a painless, left-sided, enlarging bone mass.
  • Surgical contouring was performed at 9 months of age.

Findings:

  • The surgical intervention for mandibular fibrous dysplasia was successful.
  • No evidence of recurrence or new growth was observed at 6 months post-surgery.

Implications:

  • This case highlights the possibility of early-onset mandibular fibrous dysplasia.
  • Early surgical management can be effective in treating infantile craniofacial fibrous dysplasia.
  • Long-term monitoring is necessary due to the potential for recurrence.

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