Pulmonary developmental anomaly associated with Klippel-Feil syndrome and anomalous atrioventricular conduction

We report the findings in a patient with Klippel-Feil syndrome and associated agenesis of right upper and middle lobes, hypoplasia of the right lower lobe of the lung, and Lown-Ganong-Levine syndrome. To our knowledge, such an association has not been previously described.