Related Experiment Videos
Hypoplasia of urinary bladder
J H Meriwether1, R Witherington
1Section of Urology, Medical College of Georgia School of Medicine, Augusta.
Urology
|April 1, 1992
Summary
This study details three female patients with bladder hypoplasia, a rare congenital condition. Early intervention with cutaneous ureterostomy led to survival into adulthood, with some receiving kidney transplants.
Area of Science:
- Pediatric Urology
- Congenital Anomalies
- Nephrology
Background:
- Bladder hypoplasia is a rare congenital anomaly.
- Associated congenital anomalies can complicate management.
- Obstructive uropathy is a common presentation in affected infants.
Observation:
- Three female patients with bladder hypoplasia were identified.
- All presented in early infancy with significant obstructive uropathy.
- Management involved early loop cutaneous ureterostomy.
Findings:
- All patients survived to adulthood.
- Two patients received kidney transplants into an ileal conduit.
- One patient maintained good health with cutaneous ureterostomy alone.
Implications:
- Early ureterostomy is a viable management strategy for bladder hypoplasia.
- Long-term outcomes can be favorable, including successful kidney transplantation.
- Understanding pathogenesis is crucial for improved patient care.