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Familial total ophthalmoplegia with iris transillumination (a neurocristopathy)
G W Cibis1, R C Tripathi, B J Tripathi
1Children's Mercy Hospital, University of Missouri Kansas City School of Medicine, Kansas City.
American Journal of Ophthalmology
|April 15, 1992
Abstract:
A family with total (internal and external) ophthalmoplegia had associated iris transillumination. No abnormal visual-evoked response brain lateralization indicative of albinism was found. On the basis of avian chimera experiments showing iris muscles to be derived from neural crest cells, we proposed a neurocristopathic theory to explain all clinical findings in this family.