[Telangiectatic osteogenic sarcoma]

The authors treated 6 children with sarcoma telangiectaticum (SOT). Their average ages was 7.8 years (ranging from 4 to 15 years of age). In 3 children the tumor was located in the proximal epiphysis of the femur and in the remaining 3 cases in the distal epiphysis of the femur. Clinical symptoms were present on average 8.6 weeks (ranging from 2 to 20 weeks) before the final diagnosis was made. In 3 children the final diagnosis was made after performing 1 biopsy, while in the remaining 3 cases a second biopsy was required to confirm the diagnosis. All cases were given pre-op chemotherapy (Cisplatin, Adriablastine). In all cases quick growth of the tumor was noted and in all cases a pathological fracture occurred. In 2 children mutilating surgical procedures were performed, 1 child had an endoprosthesis implanted outside our facility and 1 child was treated for lung metastases. Two children are alive, but no information about their medical condition is available.